Intracerebral small round cell tumor: An unusual case with EWS-WT1 translocation

Karim Bouchireb; Nathalie Auger; Ranjeev Bhangoo; Federico Di Rocco; Nicole Brousse; Olivier Delattre; Pascale Varlet; Jacques Grill

doi:10.1002/pbc.21648

Intracerebral small round cell tumor: An unusual case with EWS-WT1 translocation

Karim Bouchireb, Nathalie Auger, Ranjeev Bhangoo, Federico Di Rocco, Nicole Brousse, Olivier Delattre, Pascale Varlet, Jacques Grill

Résultats de recherche: Contribution à un journal › Article › Revue par des pairs

13 Citations (Scopus)

Résumé

Desmoplastic small round cell tumor (DSRCT) is a rare tumor, seen both in children and young adults with a marked predilection for the peritoneal cavity. Histology showed a small round cell tumor with a fibromyxoïd stroma and immunohistochemistry indicated neural and mesenchymal differentiation, and diagnosis was made by molecular detection of the EWS-WT1 fusion gene product. DSRCT should be considered in the differential diagnosis of intracranial small round cell tumors.

langue originale	Anglais
Pages (de - à)	545-548
Nombre de pages	4
journal	Pediatric Blood and Cancer
Volume	51
Numéro de publication	4
Les DOIs	https://doi.org/10.1002/pbc.21648
état	Publié - 1 oct. 2008

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10.1002/pbc.21648

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abstract = "Desmoplastic small round cell tumor (DSRCT) is a rare tumor, seen both in children and young adults with a marked predilection for the peritoneal cavity. Histology showed a small round cell tumor with a fibromyxo{\"i}d stroma and immunohistochemistry indicated neural and mesenchymal differentiation, and diagnosis was made by molecular detection of the EWS-WT1 fusion gene product. DSRCT should be considered in the differential diagnosis of intracranial small round cell tumors.",

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AU - Bouchireb, Karim

AU - Auger, Nathalie

AU - Bhangoo, Ranjeev

AU - Di Rocco, Federico

AU - Brousse, Nicole

AU - Delattre, Olivier

AU - Varlet, Pascale

AU - Grill, Jacques

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