Role of adjuvant radiation therapy after surgery for abdominal desmoplastic small round cell tumors

Vincent Atallah, Charles Honore, Daniel Orbach, Sylvie Helfre, Anne Ducassou, Laurence Thomas, Mihai Barbu Levitchi, Augustin Mervoyer, Salem Naji, Charles Dupin, Pauline J. Bosco-Levy, Pascale Philippe-Chomette, Guy Kantor, Benedicte Henriques De Figueiredo, Marie Pierre Sunyach, Paul Sargos

    Résultats de recherche: Contribution à un journalArticleRevue par des pairs

    25 Citations (Scopus)

    Résumé

    Purpose To identify the prognostic role of adjuvant abdominal radiation therapy (RT) on oncologic outcomes as a part of multimodal treatment in the management of desmoplastic small round cell tumor (DSRCT) and to determine its impact according to the quality of surgical resection. Methods and Materials All patients treated for primary abdominal DSRCT in 8 French centers from 1991 to 2014 were included. Patients were retrospectively staged into 3 groups: group A treated with adjuvant RT after cytoreductive surgery, group B without RT after cytoreductive surgery, and group C by exclusive chemotherapy. Peritoneal progression-free survival (PPFS), progression-free survival (PFS), and overall survival (OS) were evaluated. We also performed a direct comparison between groups A and B to evaluate RT after cytoreductive surgery. Radiation therapy was also evaluated according to completeness of surgery: complete cytoreductive surgery (CCS) or incomplete cytoreductive surgery (ICS). Results Thirty-seven (35.9%), thirty-six (34.9%), and thirty (28.0%) patients were included in groups A, B, and C, respectively. Three-year OS was 61.2% (range, 41.0%-76.0%), 37.6% (22.0%-53.1%), and 17.3% (6.3%-32.8%) for groups A, B, and C, respectively. Overall survival, PPFS, and PFS differed significantly among the 3 groups (P<.001, P<.001, and P<.001, respectively). Overall survival and PPFS were higher in group A (RT group) compared with group B (no RT group) (P=.045 and P=.006, respectively). Three-year PPFS was 23.8% (10.3%-40.4%) for group A and 12.51% (4.0%-26.2%) for group B. After CCS, RT improved PPFS (P=.024), but differences in OS and PFS were not significant (P=.40 and P=.30, respectively). After ICS, RT improved OS (P=.044). A trend of PPFS and PFS increase was observed, but the difference was not statistically significant (P=.073 and P=.076). Conclusions Adjuvant RT as part of multimodal treatment seems to confer oncologic benefits for patients treated for abdominal DSRCT after cytoreductive surgery and perioperative chemotherapy.

    langue originaleAnglais
    Pages (de - à)1244-1253
    Nombre de pages10
    journalInternational Journal of Radiation Oncology Biology Physics
    Volume95
    Numéro de publication4
    Les DOIs
    étatPublié - 15 juil. 2016

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